Diagnosis and Treatment in patient with Herlyn-Werner-Wunderlich Syndrome: A case causing pelvic pain

Background: Herlyn-Werner-Wunderlich (HWW) syndrome is a rare variant of Mullerian duct anomalies. The characteristic triad this includes didelphys uterus, obstructed hemivagina, and ipsilateral renal agenesis, recently known as Obstructed Hemivagina Ipsilateral Renal Anomaly (OHVIRA) syndrome. most common presentation abdominal pelvic pain, dysmenorrhea, mass secondary to hematocolpos, hematosalping or hematometra.Objective: determine the diagnosis operative management HWW case with pain chief complaint. Method: examination tracing medical records at Dr Sardjito Hospital Yogyakarta.Results Discussion: Fourteen-year-old female, presented pain. Physical revealed cystic in abdomen inferior, palpable up 3 cm inferior umbilicus. From Intravenous Pyelography (IVP) examination, it was found normal anatomy function right kidney, but there no left kidney. On contrast-enhanced CT scan, magnetic resonance imaging (MRI) laparoscopy showing complete duplication uterus from horn cervix connection between two uterine cavities, both ovaries were normal, fallopian tube enlarged, attached ovary, kidney found. Operative vaginal septectomy procedure performed.Conclusion: MRI accurate for providing details regarding altered identifying associated hematocolpos,hematosalping hematometra cases. Surgical intervention by performed relieve symptoms, provide better reproductive sexual functions.Keywords: syndrome; disgenesis;